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Mitochondria-targeted antioxidants and selective peroxisome proliferator-activated receptor delta (PPARδ) agonist improve bioenergetics in glutaric acidemia type 1 patient’s fibroblasts

Bianca Seminotti; Kara Sampson; Mora Ghattes; Peter Wipf; Jerry Vockley
Biochimica et Biophysica Acta (BBA) - Bioenergetics · Vol. 1865 · pp. 149480 · 2024

Abstract

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Bibliographic Information

JournalBiochimica et Biophysica Acta (BBA) - Bioenergetics
PublisherElsevier
Publication Date2024-09-01
Publication Year2024
Volume1865
Pages149480
Document TypeJournal Article
eISSN0005-2728
DOI10.1016/j.bbabio.2024.149480
SubjectAgricultural and Biological Sciences

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NARA Access Coverage1995-02-01~2025-01-01
Journal Homepagehttps://www.sciencedirect.com/science/journal/00052728
Publisher PageOpen Publisher Page
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