Human activity has altered nearly all ecosystems on Earth, contributing to substantial biodiversity loss across taxonomic, genetic and functional dimensions, from the intraspecific to the ecosystem scale. Yet some components of biodiversity remain hidden or underappreciated, including behavioural diversity. Behaviour is often among the earliest whole‐organism responses to environmental change, and diversity in behaviour can oc...

Friedreich’s ataxia (FA) is a rare, autosomal recessive neurodegenerative disease that primarily affects children and adolescents in their transition to adulthood, which is associated with several adverse life events caused by the disease progression. This article aims to describe life events associated with FA and their impact on patient-reported outcomes in pediatric and adult onsets. A newly adapted Life Events Questionnair...

Background and Objectives: Friedreich ataxia (FA) causes progressive impairment of communication due to gradual deterioration of speech, associated with impaired hearing, socio-cognitive and language skills. There is an urgent need to investigate the impact of this multiparametric alteration on patients’ lives. Therefore, the COMunication and ATAXia measure (COMATAX) was developed and validated in French and German. Methods: I...

Heatwaves (HWs) are high-impact phenomena stressing both societies and ecosystems. Their intensity and frequency are expected to increase in a warmer climate over many regions of the world. While these impacts can be wide-ranging, they are potentially influenced by local to regional features such as topography, land cover, and urbanization. Here, we leverage recent advances in the very high-resolution modelling required to elu...

The increase in computational resources has enabled the emergence of multi-model ensembles of convection-permitting regional climate model (CPRCM) simulations at very high horizontal resolutions. An example is the CORDEX Flagship Pilot Study on “Convective phenomena at high resolution over Europe and the Mediterranean”, a set of kilometre-scale simulations over an extended Alpine domain. This first-of-its-kind multi-model ense...